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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Aav-U7
Muscle strength
Satellite cells
Dysferlin
Adipose tissue
Myopathy
Skeletal muscle
Cell therapy
Lamins
Nuclear envelope
Bioinformatique
Gene therapy
Biomarker
GENE
Myoblast
Sarcopenia
Autologous
Fibrosis
Muscle fibrosis
CNOT6L
APOPTOSIS
Dystrophin
Aged
ALS
PABPN1 agregates
Calcium
FAPs
Exon-skipping
Actin
Dystrophie musculaire oculopharyngée
Myoblasts
Muscle
MUTATIONS
Myotube
Antisens oligonucleotides
Differentiation
Pax7
Functional genomics
DNA methylation
Bioinformatics
Bile salt hydrolases
CD49d
Agrégats de PABPN1
Annexin A2
Inflammation
Human
PABPN1
Ageing
Myogenesis
C2 domains
DUX4
RNA
Myositis
Geriatric assessment
AAV
Regeneration
OPMD
Haploinsufficiency
Accelerometry
Myosin
FSHD
Myopathies
Satellite cell
Transcriptomics
AChR antibodies
Anti-acetylcholine receptor antibodies
Atrophy
Andermann syndrome
Alzheimer's disease
AAV vectors
ARN
Thérapie génique
Pharyngeal muscle
Neuromuscular junction NMJ
Cross-bridge kinetics
Oculopharyngeal muscular dystrophy
Biopsies humaines
CS
BINDING SPECIFICITY
Muscle stem cells
Aggregate
C2C12 cells
Intercellular communication
DMD
Arbovirus
AUTOPHAGY
2-D PAGE
Antiserum
Gene replacement
Alphavirus
Autoimmune diseases
Anti-fibrotic pharmacotherapies
Duchenne muscular dystrophy
Xenograft
Triplet expansion disease
Metabolism
Botulinum neurotoxin
Dysferlinopathy
Akt
Muscle dystrophy